Abstract:The congenital idiopathic nystagmus is a eye disease, which is not frequently encountered disease.,These disease can find in infants or young children,especially in less than six months children,.The disease have some features such as onset time early or not determined,eye sustained jump or swing involuntarily,Akira sensation in few patients,varying degrees of visual impairment,and some vision reduced and can not be corrected,the phenomenon of lateral view or compensatory head,and some head shaking,as well as the performance of compensatory behavior such as frequent blinking.The main treatment for this disease is surgery.Many effective factors:age of onset,nystagmus intensity,compensatory head,resting eye position,vision,operation type.This paper present the recent therapy development of this disease.