·AIM:To detect the clinical characters and classification of the congenital retinal vascular anomalies.METHODS:Eleven cases(16 eyes)of congenital retinal vascular anomalies were examined by ocular examination,fundus photography and fundus fluorescein angiography(FFA).RESULTS:The congenital retinal vascular anomalies were located at the posterior pole in all cases.Congenital retinal vascular anomalies were classified as follows:congenital huge retinal macrovessel(1 case 1 eye);congenital retinal venous beading(3 cases 6 eyes),congenital retinal arteriolar tortuosity(1 case 1 eye),congenital retinal arterio-venous microvessel(2 cases 4 eyes);and congenital prepapillary vascular loops(3 cases 3 eyes);congenital retinal macrovessel(1 case 1 eye).Four cases(4 eyes)were associated with spontaneous hemorrhage induced by physical exertion.CONCLUSION:Most of the congenital retinal anomalies are located at the posterior pole,involving arteries and veins,and can be associated with spontaneous hemorrhage induced by physical exertion.They should be differentiated from the diabetic retinopathy and other retinal vascular diseases.