先天特发眼球震颤是以眼部表现为主的疾病,虽然不属于常见或多发病,但在临床上并非罕见,多见于婴幼儿,发病时间一般都在半岁以内。该病的特点为:发病早或发病时间不能确定,眼球不自主的持续跳动或摆动,极少患者有晃视感,大多数患者都有不同程度的视力损害,有的视力减低比较严重,而且不能矫正,较多患者有侧视现象和代偿头位表现,有的头部摇晃,还有的表现为频繁眨眼等代偿现象。该病的主要治疗手段是手术治疗,但影响手术效果的因素很多:发病年龄,眼震强度,代偿头位,休止眼位,视力,手术方式和手术量等。随着近年的发展,对该病有了更深入的认识,我们就一些问题做一简要回顾。

The congenital idiopathic nystagmus is a eye disease, which is not frequently encountered disease.,These disease can find in infants or young children,especially in less than six months children,.The disease have some features such as onset time early or not determined,eye sustained jump or swing involuntarily,Akira sensation in few patients,varying degrees of visual impairment,and some vision reduced and can not be corrected,the phenomenon of lateral view or compensatory head,and some head shaking,as well as the performance of compensatory behavior such as frequent blinking.The main treatment for this disease is surgery.Many effective factors:age of onset,nystagmus intensity,compensatory head,resting eye position,vision,operation type.This paper present the recent therapy development of this disease.

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