A series of fundus changes caused by excessive axial elongation in pathological myopia, especially maculopathy, are the main factors causing vision loss or blindness. In recent years, with the increasing prevalence of high myopia and pathological myopia, people pay more and more attention to the fundus complications of pathological myopia. It has become a big difficult problem to prevent the irreversible vision impairment caused by pathological myopia. The purpose of this review is to discuss the latest progress of fundus characteristics, diagnosis and treatment of maculopathy in pathological myopia from three aspects based on the latest classification of myopic maculopathy, namely ATN classification system, which considers atrophic(A), tractional(T)and neovascular(N)components.