Adenoid cystic carcinoma of lacrimal gland(LGACC)is the most common malignant epithelial tumor of the lacrimal gland, which is characterized by high recurrence rate, easy metastasis and poor prognosis. Although the current clinical treatment modalities for adenoid cystic carcinoma of lacrimal gland mainly include surgical resection, radiotherapy, and chemotherapy, its survival rate is still low. Therefore, it is particularly urgent to further study the pathogenesis of adenoid cystic carcinoma of the lacrimal gland and find out the biomarkers for adenoid cystic carcinoma of the lacrimal gland. In this paper, we will review the research progress in biomarkers of adenoid cystic carcinoma of the lacrimal gland.